Great artery relationship in DORV

What is the commonest great artery relationship in DORV?


Double outlet right ventricle (DORV) is a cyanotic congenital heart disease in which both the aorta and pulmonary artery arises from the right ventricle. There will be an obligatory ventricular septal defect as well for the left ventricular blood to flow out. Commonest great artery relationship in DORV is side by side aorta and pulmonary artery. This pattern is seen in about two thirds of the cases, with aorta to the right of the pulmonary artery. Both semilunar valves will be in the same transverse and coronal planes.

Other types of great  artery relationship in DORV are D-TGA like, NRGA like and L-TGA like.

In about a quarter of the cases of DORV, aorta is to the anterior and right of pulmonary artery (D-TGA – dextro transposition of great arteries like). This relationship is seen in Taussig-Bing anomaly with DORV, large subpulmonic ventricular septal defect, transposed great vessels, and pulmonary artery overriding the ventricular septal defect. Semilunar valves are at the same level and there is bilateral conus.

Aorta is located anterior and to the left of pulmonary artery in about seven percent of cases (L-TGA – levo transposition of great arteries like).
Rarest type of great  artery relationship in DORV is normally related great arteries (NRGA) occur in only about three percent of the cases, with aorta arising posterior and to the right of pulmonary artery.